CRETINISM.

This singular disorder was first discovered and noticed by Plater, about

the middle of the seventeenth century, among the poor inhabitants of

Carinthia and the Valais, where, as in the valleys of the Lower Alps and

the Pyrenees, it is also found to be an endemic affection. According to

Sir George Staunton, it is also observed in Chinese Tartary. It has been

erroneously confounded by some writers with bronchocele and rachitis, from

both of which it is totally distinct.

Cretinism presents various modifications in kind, and every intermediate

grade between that extreme degree of physical and mental debasement which

is characterized by the utmost deformity, and entire absence of mental

manifestation, the organic and vegetative functions only being performed.

There are certain circumstances that distinguish cretins from idiots; and

their infirmities appear to depend upon endemic or local causes, regarding

which much diversity of opinion has prevailed both amongst medical men and

travellers.

The cretins were also called _Cagots_ and _Capots_. In Navarre these

unfortunates go by the name of _Gaffos_ and _Ganets_; and in various

valleys of the Pyrenees they are called _Gezits_ or _Gezitains_. Near La

Rochelle, some of them are also found, and there they are known by the

appellation of _Coliberts_; and in Britanny _Cacons_ and _Cagneux_. The

derivation of these names shows the contempt and disgust that they

excited,--_Cagot_, according to Scaliger, being derived from _Canis

Gottus_, or _Dog of a Goth_; _Colibert_ is traced to _quasi libertus_, or

slave. The Spaniards call them _Gavachos_, a term of reproach, which they

also applied to the French during the Peninsular struggle.

The body of these poor creatures is stunted, their height not exceeding

four feet. There is a total want of due proportion between it and the

other parts, the height of the head with reference to the body being from

one-fourth to one-fifth, instead of one-eighth, the natural proportion;

the neck is strong, and bent downwards; the upper limbs reach below the

knees, and the arm is shorter than the fore-arm; the chest narrow, the

abdomen hemispherical, and of a length not exceeding the height of the

head; the thighs, with the haunches, of greater width than the shoulders,

and shorter than the legs, the calves of which are wanting; the feet and

toes distorted. In the head, the masticating organs, the lower jaw, and

the nose, preponderate considerably over the organs of sense and

intelligence; the skull is depressed, and forms a lengthened and angular

ellipsis; the receding forehead presents internally large frontal sinuses,

to which the brain has yielded part of its place; the top of the head is

flattened, instead of being vaulted; the occiput projects but slightly,

and runs almost even with the nape of the neck, as in ruminating animals.

The face is neither oval nor round, but spread out in width; the eyes are

far apart, slightly diverging, small, and deep-seated in their orbits; the

pupil contracted, and not very sensitive to light; the eyelids, except

when morbidly swollen, are flaccid and pendent. Their look is an unmeaning

stare, and turns with indifference from every thing that is not eatable.

The elongated form of the lower jaw, the thick and puffed lips, give them

a greater resemblance to ruminating creatures than to man. The tongue is

rather cylindrical than flat, and the saliva is constantly running from

the angles of their mouth. Enlargement of the thyroid glands generally

prevails, sometimes to an enormous extent. Indeed, this appearance is

commonly considered as a distinguishing sign of cretinism. The other

glands of the throat are also obstructed. Many of these poor wretches are

both deaf and dumb; yet do they appear unconscious of their miserable

existence. Stretched out or gathered up under the solar rays, their head

drooping in idiotic apathy, they are only roused from their torpor when

food is presented to them.

This endemic malady is supposed to arise from the use of snow-water, or of

water impregnated with calcareous earth. Both of these opinions are

without foundation. All the inhabitants of districts near the glaciers,

drink snow and ice waters without being subject to the disorder; and the

common waters of Switzerland, strongly impregnated with calcareous

substances, are most salubrious. At Berne, the waters are extremely pure,

yet Haller observed that swellings of the throat are not uncommon. De

Saussure has assigned another cause, and refers the disorder to the

physical features of the mountainous districts in which it prevails. The

valleys, he tells us, are surrounded with very high mountains, sheltered

from currents of fresh air, and exposed to the direct, and what is worse,

the reflected rays of the sun. They are marshy, and hence the atmosphere

is humid, close, and oppressive. When to these chorographical causes, he

further says, we add the domestic ones, which are also well known to

prevail among the poor of these regions,--such as innutritious food,

indolence, and uncleanliness, with a predisposition to the disease from an

hereditary taint of many generations,--we can sufficiently account for the

prevalence of cretinism in such places, and for the most humiliating

characters it is ever found to assume.

This specious reasoning, however, is overthrown by observation. In the

first instance, this character of the country does not affect its other

inhabitants; and secondly, the _goitre_ is found in warm latitudes, and

Mungo Park observed it amongst the Africans of Bambara, on the banks of

the Niger. Marsden has also seen it at Sumatra. Moreover, this affection

is scarcely ever seen in the mountains, but principally prevails in the

valleys.

It is more than probable that these ill-favoured creatures belong to a

particular race; for we must take care not to confound goitre with

cretinism, since goitre is common where cretinism is prevalent. It has

been remarked that the offspring of the natives of the Valais who

intermarry with persons from the Italian side of the Alps, are more

subject to goitres than those born of native parents; and that females who

have husbands from the higher Alps, seldom have children affected with

this infirmity. It is pretty clear that in these observations, goitre and

cretinism are confounded.

That these miserable cagots belong to a particular race of men, most

probably accidentally degraded in their transmission from our primitive

stock, appears most likely. We have sought the derivation of the several

terms of contempt and disgust attached to them in different countries, to

which migration may have led their parents. Some writers have traced their

descent to the Goths and Vandals, thus chastised for their devastations.

Gebelin, Belleforet, and Ramont consider them as descendants of the

Visigoths; while Marca, bishop of Couserans, denounces them at once as

Jews and Saracens; and other clerical writers have maintained that they

are the miserable relicts of the heretic Albigenses who had escaped the

holy massacres of 1215; although there did exist cagots in the year 1000,

in the abbey of St. Luc, as they are described in a _for_ of Navarre,

bearing date 1074, and issued by Ramirez.

These helpless beings have also been considered as the offspring of

Bohemians and gipsies. Bishop, or rather Senator Gregoire, maintained that

they sprung from the hordes of northern barbarians who overran the south

of Europe in the third and fourth centuries. Whatever might have been the

origin of these poor creatures, they seem to share that ignominious

destiny that has marked various races in different countries. The _Agotos_

of Navarre, the _Maragotos_ of Leon, the _Batuecos_ of Castile, the

_Wendes_ of Silesia, are all held in as much contempt as the _Parias_ and

the _Vaddahs_ of India. Even in Otaheite a degraded caste was found, from

which victims were selected to appease Divine wrath, or propitiate their

gods.

The traditional contempt in which certain races are held, a contempt that

seems to have affected their physical appearance, may perhaps be traced to

the degradation of slavery, that seems to deprive man of all his proud

attributes, both in a moral and physical point of view. The effects of

tyranny, and the distinctions that oppression has created in the several

castes and ranks of mankind, are every where evident. What a difference

exists in Scotland between the chieftains and the humbler individuals of

their clans!--between the naires of India and their vassals! In France,

said Buffon, you may distinguish by their aspect, not only the nobility

from the peasantry, but the superior order of nobility from the inferior,

these from the citizens, and citizens from the peasants. "The field-slaves

in America," observes the enlightened Dr. Smith, "are badly clothed, fed,

and lodged, live in small huts in the plantations, remote from the example

and society of their superiors. Living by themselves they retain many of

the customs and the manners of their ancestors. The domestic servants, on

the other hand, who are kept near the persons or employed in the families

of their masters, are treated with great lenity, their service is light,

they are well fed and clothed. The field-slaves, in consequence of their

condition, are slow in changing the aspect and figure of Africa; while the

domestic servants have advanced far before them in acquiring the agreeable

and regular features, and the expressive countenance, of civilized

society. The former are frequently ill-shaped; they preserve in a great

degree the African lips, and nose, and hair; their genius is dull, and

their countenances sleepy and stupid. The latter are straight and well

proportioned; their hair extends to three or four, sometimes even to six

or eight inches; the size of their mouth is handsome, their features

regular, their capacity good, and their looks animated." Dr. Prichard has

also stated that similar changes become visible in the third and fourth

generations in the West India islands; and I have seen several negresses

in those colonies perfectly beautiful. In the Bahama islands I knew a

female slave of the name of Leah, belonging to my late friend Mr.

Commissary Brookes, as black as jet, and descended in the third

generation from African parents, whose features would have vied in

symmetry with the fairest specimen of the Caucasian race.

Let us not, therefore, seek in snow-water or calcareous impregnations for

the causes of deformity and degradation in any unfortunate castes of

mankind. Their misery may more probably be traced to the iron rod of

despotism, or the oppression of bigotry,--influences that mark out races

as abject slaves, or objects of Divine wrath, that ought to be scorned by

the wealthy and the powerful, and spurned and persecuted by the faithful

and the elect; although, when it has served its purposes, priestcraft has

held up the cagot, and the leper, and the idiot, as objects of veneration.

When the tourist, in his Alpine and Pyrenean excursions, meets a wretched

cagot, let him pause and contemplate the offspring of slavery, and reflect

on what man is, and on what man might be,--nay, on what man _will_ be.

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